Dentinogenesis Imperfecta - Clinical Presentation and Management

From Volume 37, Issue 6, July 2010 | Pages 364-371

Authors

Harmeet Dhaliwal

BDS, MFDS RCS(Eng), MOrth RCS(Eng), MDentSci(Leeds)

SpR Orthodontics, Leeds Dental Institute

Articles by Harmeet Dhaliwal

Sarah McKaig

Consultant in Paediatric Dentistry, Birmingham Dental Hospital, St Chad's Queensway, Birmingham B4 6NN, UK

Articles by Sarah McKaig

Abstract

Dentinogenesis imperfecta (DI) is a hereditary condition which affects the development of dentine in both the primary and permanent dentitions. Three types of DI have been described in the literature. The presentation of DI is variable, depending on the type and severity of the disease. Early intervention in the treatment of a patient with DI is extremely important both for psycho-social and for functional reasons. This paper attempts to describe the clinical presentation and management of DI, and explores its association with certain medical conditions.

Article