Abstract
Congenital insensitivity to pain is a rare condition present from birth. To date, congenital insensitivity to pain has been described in groups of hereditary sensory and autonomic neuropathies (HSAN). Within the HSAN group there are five conditions described. This case report describes the management of a female with congenital insensitivity to pain up to her present age of six years. The aim of treatment was to prevent episodes of oro-facial trauma and self-mutilation injuries. The primary teeth were removed on eruption and further management of the permanent dentition has involved the use of soft occlusal guards together with behaviour management techniques, including an educational component.